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Table 1:

Descriptive analysis of patients with DW with brainstem involvement

Variable
Sex (No.) (%)
 Male29 (39.7%)
 Female44 (60.3%)
Age
 Age (mo)25 mo (IQR = 10 days to 15.6 mo)
Birth status (No.) (%)
 Premature20 (27.4%)
 Full-term35 (47.9%)
 Unknown18 (24.7%)
Imaging features (No.) (%)
 Severe macrocrania24 (32.9%)
 Extreme vermian hypoplasia12 (16.4%)
 Cerebellar dysplasia27 (37%)
 Anteroposterior disproportion67 (91.8%)
 Hydrocephalus43 (58.9%)
 Corpus callosum agenesis37 (50.7%)
 Interhemispheric cyst11 (15.1%)
 Gray matter migration18 (24.7%)
 Calcification or hemorrhage12 (16.4%)
 Fastigial recess angle (mean)167.1° (SD, 46.6°)
 Posterior fossa perimeter (mean) (mm)172.4 (SD, 110.6)
Clinical features (No.) (%)
 Seizure31 (42.5%)
 Artificial airway dependency32 (43.8%)
 Enteral feeding tube dependency40 (54.8%)
 Mortality15 (20.5%)