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Comparison between KTS and Parkes-Weber Syndrome3

KTSParkes-Weber Syndrome
Cutaneous vascular malformationAlmost invariably tends to be dark; may be verrucousFrequent; usually a pink capillary malformation
Arteriovenous fistulasNot significantInvariablea
Deep veinCommonaAbsent
Lateral venous anomalyCommonaAbsent
GigantismUsually disproportionate with soft-tissue thickening predominating; often giant toes presentUsually proportionate
Lengthening of limbUsually minorOften minor
Associated lesionsCommonRare
LymphaticsOften hypoplasticUsually hyperplastic
PrognosisGood; stable after childhoodMay be progressive deterioration
  • a Indicates signs present in our case.