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Table 2:

Correlation of disease severity and CNS volumes with disease duration and CAG repeat length

Disease DurationCAG Repeat Length
SCA3SCA6SCA3SCA6
ICARS scoreρ = 0.598ρ = 0.632N.S.N.S.
P = .011aP = .006b
Cerebellar volumeρ = −0.506ρ = −0.623N.S.N.S.
P = .038aP = .017a
Brain stemρ = −0.51N.S.N.S.N.S.
volumeP = .036a
  • a Significant with P < .05.

  • b Highly significant with P < .01.