Table 1:

Inner ear imaging findings in patients included in this study^{^a}

Patient	Age at MRI/CT	Cochlea	Cochlear Nerve	Vestibule	Posterior SCC	Superior SCC	Lateral SCC
A	?/?	Flattened	Present	Enlarged	Agenesis	N	Large arch, thin
B	32 mo/32 mo	Small	Present	Enlarged	Small arch, thick	Large arch, thin	Large arch, thin
C	32 mo/32 mo	Small	Present	Enlarged	Small arch, thick	N	Small arch, thick
D1^{^b}	5 wk/–	Small, flattened	Present	Enlarged	Small arch, thick	Small arch, thick	Small arch, thick
D2^{^b}	2 mo/2 mo	Small, flattened	Present	Enlarged	N	R: small arch, thick L: N	Small arch, thick
E	3 yr/3 yr	Flattened	Present	Enlarged	Agenesis	Agenesis	R: agenesis; L: small arch, thick
F	2 mo/–	Small, flattened	Absent	Enlarged	Agenesis	Agenesis	R: agenesis; L: small, thin
G	5 yr/5 yr	Flattened	Present	Enlarged	Agenesis	Agenesis	Agenesis
H	18 yr/–	Small, flattened	R: present; L: present, thin	Enlarged	Agenesis	Agenesis	Small, thin
I	20 mo/20 mo	Small, flattened	Present	Enlarged	Agenesis	Small arch, thick	R: small, thin, incomplete; L: small, thin
J	4 yr/4 yr	Small, flattened	R: present; L: absent	Enlarged	Agenesis	Agenesis	Agenesis
K	18 mo/18 mo	N	Present	Enlarged	Agenesis	Agenesis	Small, thin
L	–/16 yr	Small	N/A	R: enlarged; L: N	Small arch, thick	Agenesis	Small arch, thick
M	8 days/ 8 days	Small, flattened	Absent	Enlarged	Agenesis	Agenesis	Agenesis
N	31 yr/31 yr	Flattened	Present	Enlarged	Agenesis	Small arch, thick	Small arch, thick
Agenesis or absence (%)			21		67	53	33
Defect (%)		93	29	100	93	87	100

Note:—N indicates normal; N/A, could not be analyzed; R, right; and L, left; –, not performed; ?, age unknown.
↵a When right or left is not specified, the same findings were observed in both sides. In the case of an asymmetric defect, the percentage of absence and/or defects was calculated on the basis of the more severe side.
↵b Brothers.