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Table 2:

Brain vascular malformation phenotypes of 75 subjects with HHT

Capillary Vascular Malformation
012+
0 AVMs/AVFs1 (1%)a17 (23%)18 (24%)b
1 AVM20 (27%)5 (7%)3 (4%)
2 AVMs1 (1%)0 (0%)1 (1%)
1 AVF4 (5%)1 (1%)0 (0%)
2 AVFs1 (1%)1 (1%)0 (0%)
1 AVM and 1 AVF2 (3%)0 (0%)0 (0%)
  • a This individual had 1 dural arteriovenous fistula only.

  • b One individual in this group had a developmental venous anomaly.