1naresh2naresh
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Total Sample (n = 37) Demographic characteristics Female (No.) (%) 21 (56.8) Age at moyamoya diagnosis (median) (IQR, 25–75) (yr) 10 (6.3–11.8) Age at initial CVR (median) (IQR, 25–75) (yr) 10.7 (7.5–14.7) Time to follow-up (median) (IQR, 25–75) (mo) 20.8 (13.7–84.1) Moyamoya classification Idiopathic 14 (37.8) Syndromic 23 (62.2) NF1 9 (24.3) Trisomy 21/other chromosomal disorders 7 (18.9) Sickle cell disease 5 (13.5) Postradiation vasculopathy 2 (5.4) Clinical presentation Stroke (No.) (%) 12 (32.4) Bilateral 2 (5.4) Right 6 (16.2) Left 4 (10.8) TIA (No.) (%) 8 (21.6) Seizure (No.) (%) 3 (8) Headaches (No.) (%) 8 (21.6) Asymptomatic (No.) (%) 6 (16.2) Other (No.) (%) 2 (5.4) Radiographic findings (No.) (%) Parenchymal Not ischemic 8 (21.6) Watershed 12 (32.4) Deep white matter 1 (2.7) Cortical 12 (32.4) Cortical 3 (8.1) Cortical ischemic and watershed 14 (37.8) Vascular Moyamoya laterality (No.) (%) Left 8 (21.6) Right 6 (16.2) Bilateral 23 (62.2) Grade of stenosis (No.) (%) 50%–74% Occlusion 5 (13.5) ≥75% Occlusion 32 (86.5)
Note:—NF1 indicates neurofibromatosis type 1.