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Table 1:

Baseline clinical and demographic characteristics

Total Sample (n = 37)
Demographic characteristics
Female (No.) (%)21 (56.8)
Age at moyamoya diagnosis (median) (IQR, 25–75) (yr)10 (6.3–11.8)
Age at initial CVR (median) (IQR, 25–75) (yr)10.7 (7.5–14.7)
Time to follow-up (median) (IQR, 25–75) (mo)20.8 (13.7–84.1)
Moyamoya classification
 Idiopathic14 (37.8)
 Syndromic23 (62.2)
  NF19 (24.3)
  Trisomy 21/other chromosomal disorders7 (18.9)
  Sickle cell disease5 (13.5)
  Postradiation vasculopathy2 (5.4)
Clinical presentation
 Stroke (No.) (%)12 (32.4)
  Bilateral2 (5.4)
  Right6 (16.2)
  Left4 (10.8)
 TIA (No.) (%)8 (21.6)
 Seizure (No.) (%)3 (8)
 Headaches (No.) (%)8 (21.6)
 Asymptomatic (No.) (%)6 (16.2)
 Other (No.) (%)2 (5.4)
Radiographic findings (No.) (%)
 Parenchymal
  Not ischemic8 (21.6)
  Watershed12 (32.4)
   Deep white matter1 (2.7)
   Cortical12 (32.4)
 Cortical3 (8.1)
 Cortical ischemic and watershed14 (37.8)
 Vascular
  Moyamoya laterality (No.) (%)
   Left8 (21.6)
   Right6 (16.2)
   Bilateral23 (62.2)
 Grade of stenosis (No.) (%)
 50%–74% Occlusion5 (13.5)
 ≥75% Occlusion32 (86.5)
  • Note:—NF1 indicates neurofibromatosis type 1.